An Adult Case of Idiopathic Pulmonary Hemosiderosis Associated with Pulmonary Fibrosis and Emphysematous Change

Masato Kono; Yuiko Oshima; Megumi Katsumata; Ryutaro Hirama; Kenichiro Takeda; Yasutaka Mochizuka; Akari Tsutsumi; Hideki Miwa; Yoshihiro Miki; Dai Hashimoto; Yoshiro Otsuki; Takafumi Suda; Hidenori Nakamura

doi:10.2169/internalmedicine.1663-23

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An Adult Case of Idiopathic Pulmonary Hemosiderosis Associated with Pulmonary Fibrosis and Emphysematous Change

Masato Kono, Yuiko Oshima, Megumi Katsumata, Ryutaro Hirama, Kenichiro Takeda, Yasutaka Mochizuka, Akari Tsutsumi, Hideki Miwa, Yoshihiro Miki, Dai Hashimoto, Yoshiro Otsuki, Takafumi Suda, Hidenori Nakamura

著者情報

キーワード: Idiopathic pulmonary hemorrhage, Diffuse alveolar hemorrhage, Pulmonary fibrosis, Emphysematous change

ジャーナルオープンアクセス早期公開

論文ID: 1663-23

DOI https://doi.org/10.2169/internalmedicine.1663-23

この記事には本公開記事があります。

The final version of this article is now available: Vol. 63 (2024), No. 1 pp. 119-124

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抄録

A 48-year-old woman was admitted to our hospital with acute respiratory failure. Chest computed tomography showed ground-glass opacity and patchy emphysematous lesions in both lungs. Corticosteroid therapy was effective; however, the disease worsened with the tapering of corticosteroids. Bronchoalveolar lavage revealed hemosiderin-laden macrophages, and video-assisted thoracic surgery showed diffuse interstitial fibrosis with diffuse alveolar hemorrhage (DAH). There was no evidence of vasculitis nor autoimmune diseases. This patient was diagnosed with idiopathic pulmonary hemosiderosis (IPH) that progressed to end-stage pulmonary fibrosis despite treatment. Autopsy demonstrated DAH with pulmonary fibrosis and emphysematous change, suggesting IPH-related pulmonary lesions.

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