von Recklinghausen's disease has been autosomal dominant inherited syndrome characteristized by generalized multiple pigmentation and neurofibroma.
The oral manifestation of von Recklinghausen's disease is relatively infrequent. A 33year-old woman with a typical case of neurofibroma in the median lingual gingiva of the mandible associated with mandibular deformity was reported. Under local anesthesia, the intra-oral tumor and the skin tumor of the right mandibular angle region were excised at the same time. In the histopathological findings, both of these tumors were revealed neurofibroma.
