抄録
An autopsy case of a 45-year-old male with Hand-Schüller-Christian's disease is reported. He had chief complaints of coughing, expectoration of sputa and general fatigability, accompanying incomplete diabetes insipidus. On chest X-ray films diffuse pulmonary fibrosis which progressed gradually was demonstrated. Biopsy specimen of the lung revealed diffuse interstitial fibrosis with occasional presence of histiocytes. At autopsy the pulmonary lesion was proved to be diffuse interstitial fibrosis with histiocytic infiltration which was a pulmonary manifestation of Hand-Schüller-Christian's disease. From the findings of the lung at biopsy and autopsy, the pulmonary lesion seemed to be a diffuse interstitial fibrosis even in the early phase.
Therefore, Hand-Shüller-Christian's disease should be included in the differential diagnosis of the diffuse interstitial pulmonary fibrosis.
