Three patients (case 1,2,3) with cor triatriatum were operated successfully. Preoperative diagnosis was established by cardiac catheterization, angiography and/or echocardiography. All cases were associated with atrial septal defect, connecting the accessory chamber in case 1 and 2, and the true chamber of left atrium in case 3. A excision of the abnormal membrane in left atrium and closure of atrial septal defect were carried out through the right atrial approach. The operation were elective in case 1, and urgent in case 2 and 3 because of pulmonary hypertension and congestive heart failure. The clinical features and hemodynamics in this anomaly are characterized by size and localization of the communication between accessory and true left atrium. Satisfactory operative results can be achieved by a complete excision of the abnormal membrane in the left atrium, based on a correct preoperative diagnosis.