Fitz-Hugh-Curtis症候群に特徴的とされる肝表面癒着を認めたMayer-Rokitansky-Küster-Hauser症候群の一例

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Background: Fitz-Hugh-Curtis syndrome (FHCS) is a condition of perihepatitis associated with gonococcal or chlamydial infection, characterized by perihepatic adhesions between the liver capsule and the diaphragm or the anterior peritoneal surface. The possibility of women with Mayer-Rokitansky-Küster-Hauser syndrome (MRKHS) experiencing sexually transmitted diseases is very low. We report a rare case where a woman with MRKHS was detected with perihepatic adhesions accidentally during laparoscopic surgery.

Case report: A 73-year-old virgin patient, who had established MRKHS, presented with right ovarian tumor. Magnetic resonance imaging revealed dermoid cyst of the right ovary and we performed laparoscopic surgery. Surgery was successful, but we found violin-string adhesions between the liver capsule and the anterior peritoneal surface. The serum tested negative for chlamydial IgA and IgG.

Comment: This case shows that perihepatic adhesions can occur because of reasons other than gonococcal or chlamydial infections.