Abstract
Intracranial teratomas are relatively uncommon and most of them are found in the pineal or the parapineal regions. Germinomas are the most common histological type of intracranial germ cell tumors. A fourth ventricular tumor composed of a teratoma with an overgrowth of striated muscle tissue and germinoma in a 12-year-old girl is reported. It is suggested that primary intracranial rhabdomyosarcomas are closely related to a teratoid origin.