Neonatal Orbital Teratoma with Intracranial Extension

—Case Report—

Abstract

Congenital teratoma of the orbit is a rare tumor, which usually manifests unilateral proptosis in an otherwise normal newborn infant. It rarely extends intracranially. A rare case of congenital orbital teratoma with intracranial extension, which presented microphthalmia from birth, is reported. Intracranial approach with orbital unroofing enabled total removal of this rare tumor during the neonatal period through combined efforts of neurosurgery and ophthalmology.