Nonfamilial Turcot Syndrome Presenting with Astrocytoma —Case Report—

Hideichi TAKAYAMA; Katsuji NAKAGAWA; Satoru ONOZUKA; Yukio IBATA; Youichi SHINOMIYA; Katsuroh HARUYAMA; Shigeo TOYA

doi:10.2176/nmc.29.606

Nonfamilial Turcot Syndrome Presenting with Astrocytoma

—Case Report—

Hideichi TAKAYAMA, Katsuji NAKAGAWA, Satoru ONOZUKA, Yukio IBATA, Youichi SHINOMIYA, Katsuroh HARUYAMA, Shigeo TOYA

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Keywords: Turcot syndrome, glioma-polyposis syndrome, cerebral astrocytoma, colonic polyposis, colonic adenocarcinoma

JOURNAL FREE ACCESS

1989 Volume 29 Issue 7 Pages 606-609

DOI https://doi.org/10.2176/nmc.29.606

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Abstract

A nonfamilial case of Turcot syndrome (glioma-polyposis syndrome) is described. A 16-year-old male with no siblings first developed a frontal astrocytoma, and was later found to have colonic polyposis with adenocarcinoma. The family history was negative for the syndrome, but his parents were first cousins.

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