Abstract
A 32-year-old female presented with an uncommon primary Ewing''s sarcoma of the skull involving the middle cranial fossa with an extremely unusual extension into the cerebral parenchyma. She was treated with surgical excision, irradiation, and chemotherapy. Two years after surgery she demonstrated no evidence of local recurrence or distant metastasis. Ewing''s sarcoma of the skull may achieve a better survival rate under adequate management than this lesion in other sites.