2026 年 13 巻 p. 295-299
Currarino syndrome is a rare congenital disorder characterized by a triad of sacral agenesis, presacral mass, and anorectal malformation. Although it is typically diagnosed in infancy or childhood, adult presentation is rare and poses unique diagnostic and surgical challenges. We present the case of a 45-year-old woman diagnosed with Currarino syndrome during pregnancy after incidental discovery of a presacral mass associated with tethered spinal cord and sacral agenesis. Over time, the mass enlarged, causing rectal obstruction and abdominal pain. A combined neurosurgical and gastrointestinal surgical approach was used to perform tethered cord release and mass resection without cerebrospinal fluid leakage, owing to autologous omental flap placement. There were no postoperative complications except for transient urinary retention and numbness in the left foot. Adult cases of Currarino syndrome require individualized, multidisciplinary surgical management. A combined neurosurgical and gastrointestinal surgical approach, incorporating preventive techniques such as autologous omental flap placement, can result in favorable outcomes with minimal complications.