A 16-year-old man was admitted because of recurrent acute pancreatitis after eating fatty foods. He denied abuse of alcohol and other drugs. The levels of serum triglyceride and cholesterol were extremely low. Transabdominal ultrasonography showed no gallstones but signs of early chronic pancreatitis. Endoscopic retrograde pancreatography via the minor papilla revealed that the dorsal pancreatic duct communicated with the loop-shaped meandering dorsal pancreatic duct, which ruled out pancreas divisum. No mutation associated with hereditary pancreatitis was found in the PRSS1 and SPINK1 genes. MMPD has been reported as a relevant factor in the onset of idiopathic recurrent acute pancreatitis. In this case, MMPD might have been relevant to recurrent acute pancreatitis and development of early chronic pancreatitis.
