抄録
We report a case of Landau-Kleffner syndrome with bilateral moderate peripheral hearing loss. Her hearing loss became apparent at age of 3. ABR showed 40∼45 dB threshold elevation. She was given hearing aid fitting and auditory training. At age of 5 years, suddenly she did neither respond to speech sounds nor speak words. She could recognize environmental sounds, but neither verbal stimulus nor melodies. EEG showed bilateral difused spike and wave complex. Though anticonvulsants were prescribed for her, her signs continued and she entered a school for deafness. At age of 7 years she gradually began to speak words again. Now she is 13 years old. Both central hearing disorders and inner speech disorders still continue. Auditory comprehension is severely impaired and so she has severe language retardation. We consider that her language disorders would be caused by both peripheral hearing loss and the central auditory and inner speech disorders.
