Decrease of Urinary Acid Mucopolysaccharides in Hurler's Syndrome after Plasma Infusion

Abstract

The fresh plasma infusion in patients affected by Hurler, Scheie or Morquio syndromes was followed by a decreased urinary excretion of chondroitin sulfate B or keratosulfate. Furthermore, in all of the patients the infusion was followed by an increased excretion of the noncetylpyridinium chloride precipitates.