Internal Medicine
Online ISSN : 1349-7235
Print ISSN : 0918-2918
ISSN-L : 0918-2918

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Multiple Myeloma Presenting with Autoimmune Autonomic Ganglionopathy
Yoshiki NakaeMizuki HyugaWataru KishimotoAkiko FukunagaSumie TabataYoshitomo MaesakoNobuyoshi ArimaYuta TeradaKenichi KomatsuOsamu HiguchiShunya Nakane
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ジャーナル オープンアクセス 早期公開

論文ID: 9096-17

この記事には本公開記事があります。
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Autoimmune autonomic ganglionopathy is an autonomic disorder that occurs as a symptom of paraneoplastic neurological syndrome. To date, there have been no reports on multiple myeloma with autoimmune autonomic ganglionopathy. A 37-year-old Japanese woman suffered from orthostatic hypotension was diagnosed with multiple myeloma (IgG kappa type), and a serological examination revealed the presence of anti-ganglionic nicotinic acetylcholine receptor (anti-gAChR) antibodies. She was treated for multiple myeloma, as a result, the autonomic disturbance improved and her anti-gAChR antibody titer decreased to undetectable levels, despite the fact that she only achieved a partial remission of multiple myeloma. Treatment for multiple myeloma may improve autoimmune autonomic ganglionopathy.

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© 2017 by The Japanese Society of Internal Medicine
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