膵管胆道合流異常症候群の病型分類に関する考察 : 先天性胆道拡張症の病因とも関連して

抄録

Anomalous pancreato-choledochal ductal junction (APCDJ) syndrome has become the matter of the interest concerning the etiology and pathogenesis of various biliary and pancreatic diseases. We classified this APCDJ into two types. Type I consists of long common channel formation which includes the majority of cases with APCDJ. Type II consists of other miscellaneous anomalous junctions. Furthermore Type I was divided into three subtypes. Type la consists of cystic dilatation of common bile duct. Type Ib consists of fusiform dilatation of common bile duct. Type la and Ib has been called as congenital biliary dilatation. The etiology of the dilatation of biliary tract in Type la and Type Ib is explained by the stricture of bile duct associated with these APCDJ, which based on our radiological and experimental studies. Type Ic consists of no dilatation of biliary tract, which was found in some cases of biliary tract carcinoma.