生涯教育講座
皮膚弾力線維異常症 臨床と病態
2003 年 113 巻 2 号 p. 127-133
詳細
2003 年 113 巻 2 号 p. 127-133
Elastic fibers are fibrous proteins in the dermis, then include elastin, fibrillins and microfibril-associated glycoproteins. Typical cutaneous disorders in which elastic fibers are primarily involved are pseudoxanthoma elasticum, actinic elastosis, cutis laxa, elastosis perforans serpiginosa, middermal elastolysis, and pseudoxanthoma elasticum-like papillary dermal elastolysis. Recent advances in the molecular pathology of these disorders were presented.
