The auditory intelligibility of the distorted monosyllables and words were studied in nomal children. Four conditions of distortion were of expansion (1.5, 2 and 3 times) and compression (0.7, 0.5 and 0.25 times) of frequency and time compoennts, respectvely. The subjects consisted of 160 children, half boys and half girls, aged 4 to 11 years, including 10 subjects in each age and sex group, and 10 young adults. The results were as follows: 1) Frequency-expanded and -compressed tests The greater the rate of expansion and compression, the poorer the intelligibility was in all subjects. When the age advanced, the intelligibility scores improved up to a certain extent in each test. Especially, it was found that the difference was signifficiant in intelligibility scores between the age of 9 and 10 years. 2) Time-expanded and -compressed tests Discrimination of all three types of time-expanded words was good and the intelligibility scores ranged above 70%. The time-compressed words at the conditions of 0.7 and 0.5 times were also discriminated well. On the contrary, the intelligibility scores at the condition of 0.25 time decreased steeply to around 50%. With increasing age, the intelligibility improved gradually without significant differerence between any ages. At the present test, there was no significant difference in intelligibility scores between boys and girls.
Four congenital syndromes of skeletal anomalies associated with deafness were described in this paper. Klippel-Feil's syndrome and Goldehar's syndrome were congenital diseases which showed cervical deformities and occasionally associated with hearing impairment. Deafness in these two syndromes were not only conductive but also sensorineural hearing loss in type. Fanconi's anemia syndrome and Madelung's deformity were the diseases which manifested congenital abnormalities on arm or finger. Deafness in these two syndromes were conductive type in most instances.
Temporal bones from a case of congenital atresia of the external auditory canal were histologically studied and reported. A 14 days old female infant died of aspiration pneumonia following upper respiratory distress due to marked hypoplasia of the mandibule. Malformations were found in the external as well as middle ears. The right external ear canal was occluded by a bony atresia plate which was a part of the squamous or tympanic bone. The canal of the left ear was filled with fibrous connective tissue. The middle ear anomalies included hypoplastic epitympanum, absence of the cochleariform process, anomalous course of the tensor tympani musle, misshaped malleus and incus, missing lenticular process, fixation of the short process of the incus, bony fusion of the malleus with the medial wall of the tympanic cavity, foot plate fixation and persistent stapedial artery. The bony and membranous labyrinths appeared normal, except the presence of the cyst-like structures in the crista of the left anterior and posterior ampullae and concretion in the base of the stria vascularis. The findings may be indicaticative of genetic disorder of the inner ear.