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Volume 39, Issue 1
Displaying 1-14 of 14 articles from this issue
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[in Japanese]2007 Volume 39 Issue 1 Pages 2
Published: January 01, 2007
Released on J-STAGE: December 15, 2011
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[in Japanese]2007 Volume 39 Issue 1 Pages 3-4
Published: January 01, 2007
Released on J-STAGE: December 12, 2011
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[in Japanese], [in Japanese]2007 Volume 39 Issue 1 Pages 5-17
Published: January 01, 2007
Released on J-STAGE: December 15, 2011
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Shoko Mano, Hiroyuki Uno2007 Volume 39 Issue 1 Pages 19-24
Published: January 01, 2007
Released on J-STAGE: December 12, 2011
JOURNAL FREE ACCESSPrevious studies have revealed that mothers of children with attention-deficit/hyperactivity disorder (AD/HD) have an authoritarian parenting style. However, the psychological process of developing an authoritarian parenting style has yet to be clearly defined. To clarify this psychological process, the present study examined the hypothesis that the characteristic behaviors of children with AD/HD initially increase the mothers' parenting stress, which influences their parenting style. Thirty-six mothers of children with AD/HD (children's mean age: 8.1 years) and the same number of controls (children's mean age: 8.4 years) participated in the present study. The mothers' parenting stress was assessed using the Japanese Parenting Stress Index. Parenting styles were assessed using the TK-style scale for evaluating the relationships between parents and children. The results indicated that the mothers of children with AD/HD had significantly higher scores than controls for all parenting stress items and negative parenting style variables (dissatisfaction, reproach, strictness, interference, inconsistency and disagreement of 10 attitudes). Stepwise multiple regression analysis revealed that the characteristic behaviors of children with AD/HD were associated with the degree of attachment in mothers, which was related to the strict and reproachful parenting style in the AD/HD group. These results suggest that mothers of children with AD/HD are likely to have a strict and reproachful parenting style as a result of a lack of attachment with the child.View full abstractDownload PDF (940K) -
Hideo Enoki2007 Volume 39 Issue 1 Pages 27-31
Published: January 01, 2007
Released on J-STAGE: December 12, 2011
JOURNAL FREE ACCESSThe author presents a case of brain death caused by salmonella encephalopathy in a 1-year-old girl. Thepatient suffered from fever, convulsive status, and coma. On the 5th day, her respiration was arrested. At that time, we confirmed the absence of brainstem reflexes. An electroencephalogram (EEG) showed a flat pattern. Only wave I was recordable in auditory brainstem responses (ABR). On the 6th day, we obtained a flat EEG and a disappearance of all components of ABR. A simultaneous elevation of her heart rate and blood pressure was observed 14 to 18 hours after the respiratory arrest. This phenomenon was equivalent to the Cushing reflex, which represents an autoregulation against increased intracranial pressure. Our case suggested that the activity of a part of the brainstem was preserved in spite of the absence of activities in EEG, ABR and brainstem reflexes at 14 hours after the onset of apnea.View full abstractDownload PDF (681K) -
Keiko Koterazawa, Kanako Nakano, Hiroyoshi Miyata, Makoto Nabetani, So ...2007 Volume 39 Issue 1 Pages 32-36
Published: January 01, 2007
Released on J-STAGE: December 12, 2011
JOURNAL FREE ACCESSWe retrospectively investigated the incidence, neuroimaging findings, and motor and intellectual disabilityof infants with cerebral palsy (CP) who were born between 1983 and 1997. The incidence of CP was found to have increased gradually and the major cause was periventricular leukomalacia. The prognosis of preterm infants was better than that of term infants.
These findings suggest that the increase in the incidence of CP has been due mainly to changes in medical care for neonates.View full abstractDownload PDF (1815K) -
Yasuhisa Toribe, Koji Tominaga, Kana Ogawa, Yasuhiro Suzuki2007 Volume 39 Issue 1 Pages 38-43
Published: January 01, 2007
Released on J-STAGE: December 12, 2011
JOURNAL FREE ACCESSWe encountered an 11-year-old girl with mitochondrial myopathy, encephalopathy, lactic acidosis, and stroke-like episodes (MELAS) who developed occipital lobe epilepsy at the age of 7 years and 4 months. Thereafter she had repeated status epilepticus associated with stroke-like episodes. Status epilepticus consisted of repetitive complex partial seizures with or without secondarily generalized tonic clonic seizures. The seizures did not respond to conventional anticonvulsive drugs, including diazepam, midazolam, phenytoin, lidocaine, chloral hydrate, and thiamylal sodium, and lasted for several hours (mean 9.5 hours). At the age of 11 years, intravenous infusion of L-arginine (0.5g/kg body weight) was first given five hours after the onset of status epilepticus.T he seizures and electroencephalographica bnormalities improved dramatically. After the introduction of L-arginine, in addition to shortened duration of status epilepticus (mean 3 hours), clinical recovery from the status epilepticus was prompt, and the average hospitalization periods could be shortened. There were no obvious adverse effects, including vomiting, hypotension, and urticaria. Our experience suggests that early intravenous administration of L-arginine may be useful in the treatment of status epilepticus associated with stroke-like episode in patients with MELAS.View full abstractDownload PDF (1955K) -
Koki Nikaido, Takahiro Kato, Rumiko Takayama, Toshiaki Doi2007 Volume 39 Issue 1 Pages 44-48
Published: January 01, 2007
Released on J-STAGE: December 12, 2011
JOURNAL FREE ACCESSA six month-old female infant developed dyspnea when she was treated with valproate sodium (VPA) and zonisamide (ZNS) for epileptic spasms. Two weeks after its onset, her dyspnea was exacerbated by respiratory syncytial virus (RSV) infection. We diagnosed interstitial pneumonitis (IP) based on her chest CT and high serum concentrations of KL-6 and surfactant protein D. Her dyspnea improved with the treatment which included steroids, neutrophil elastase inhibitor and discontinuation of VPA and ZNS. An allergic reaction probably explains the IP in our patient because steroids were effective. Her IP might have been exacerbated by several factors including the use of two anticonvulsants (VPA, ZNS), RSV infection, and physiological low serum IgA level of infants. Drug-induced interstitial lung disease should be remembered as a possible complication of anticonvulsant treatment, such as VPA and ZNS.View full abstractDownload PDF (1758K) -
Keiko Okumura, Tomohiko Tsuru, Kouichi Aizaki, Bunshiroh Akikusa2007 Volume 39 Issue 1 Pages 49-53
Published: January 01, 2007
Released on J-STAGE: December 15, 2011
JOURNAL FREE ACCESSWe report a 13-year-old boy with cerebral autosomal dominant arteriopathy with subcortical infarcts and leukoencephalopathy (CADASIL) at an early stage. He showed migraine, cognitive deficits, depressive episodes and areas of white matter hyperintensity on MRI. There were no first-degree relatives accompanied with similar symptoms. T2-and fluid-attenuated inversion recovery (FLAIR)-weighted brain MRI revealed areas of apparently symmetric high intensity in the deep white matter and periventicular caps. On ultrastructural studies of the biopsied skin, there were free granular osmiophilic materials (GOM) between vascular smooth muscle cells in the cutaneous vessels. But there were no excavations in the cell membranes that contained GOM. On immunostaining with Notch3 monoclonal antibodies, granular staining was not observed in vessels of the skin. No mutation was detected on DNA analysis of the Notch3 gene (exon 4 and part of exon 5) in peripheral leukocytes. Although the frequencies of migraine episodes and depressive episodes decreased with amitriptyline and ibuprofen, the cognitive deficits (delayed-recall impairment) and areas of white matter hyperintensity on MRI have been unchanged for the past four years.View full abstractDownload PDF (3043K) -
An Autopsy CaseIchiro Kuki, Kiyotaka Tomiwa, Shin Okazaki, Hiroko Ikeda, Hisashi Kawa ...2007 Volume 39 Issue 1 Pages 54-58
Published: January 01, 2007
Released on J-STAGE: December 12, 2011
JOURNAL FREE ACCESSWe report a 5-year-old autopsy case of late infantile type of GM1 gangliosidosis, which developed rare respiratory and intestinal complications. Obstructive apnea by adenoidal hypertrophy was improved by adenoidectomy, but the right bronchus was compressed by hilar lymph node swellings. The lymph nodes could not be treated surgically because of her poor general condition. There was hyperplasia showing foamy histiocyte including mucopolysaccharide which demonstrated a vacuolar formation containing irregular arranged fibrillar material on electron microscopy. Cerebral atrophy progressed gradually, and epileptic apnea developed, which was intractable to all antiepileptic drugs administered. Glycolipid accumulation, showing membranous cytoplasmic body on electron microscopy, seemed to lead to neurodegeneration. Abdominal distension due to hepatosplenomegaly, common bile duct dilatation compressed by lymph node swelling of the caput pancreatis part, and enteroparalysis was uncontrolled. These findings suggest that severe glycolipid deposition in lymphoreticular organs can induce various complications in patients with late infantile type of GM1 gangliosidosis.View full abstractDownload PDF (2906K) -
Yoshihiko Imamura, Yoshinao Fujikawa, Hirofumi Komaki, Eiji Nakagawa, ...2007 Volume 39 Issue 1 Pages 59-62
Published: January 01, 2007
Released on J-STAGE: December 12, 2011
JOURNAL FREE ACCESSMöbius syndrome is a rare disorder characterized by congenital bilateral facial nerve palsy. Abducent palsy or other cranial nerve palsy, facial malformations, limb malformations, and skeletal malformations are common features associated with this syndrome. We report a 9- month-old infant in whom congenital muscular disorder was previously suspected because of facial muscle involvement (mask-like face), respiratory and swallowing disturbances, and hypotonia since birth. After an improvement in the respiratory infection, she showed slightly exaggerated deep tendon reflexes and an improvement in muscle tone. The occurrence of combined facial nerve palsy, glossopharyngeal nerve palsy, vagus nerve palsy, and hypoglossal nerve palsy strongly suggested that she had Möbius syndrome. Finally, the absence of the roots of bilateral facial nerves on an MRI confirmed that the disorder was Möbius syndrome. We propose that a thin slice MRI should be obtained to observe the cranial nerves around the brain stem if patients show symptoms of congenital myopathy or congenital myotonic dystrophy as well as facial nerve and other cranial nerve paralyses.View full abstractDownload PDF (1450K) -
Ushio Ohtaki, Tomohide Goto, Sahoko Miyama2007 Volume 39 Issue 1 Pages 63-65
Published: January 01, 2007
Released on J-STAGE: December 12, 2011
JOURNAL FREE ACCESSWe report a case with dysgenesis of the carotid artery associated with congenital Horner syndrome. A 6-year-old boy, who had undergone surgical repair for pulmonary atresia, ventricular septal defect, and patent ductus arteriosus at 20 months of age, presented with miosis of the left eye, and anhidrosis of the left face, neck, and shoulder girdle. Since the anhidrosis was obvious in early childhood, he was suspected as having congenital Horner syndrome. Cranial and cervical CT showed unpredicted abnormalities of the left carotid arteries, including the absence of an internal carotid artery (ICA), and hypoplasia of the common carotid and external carotid arteries. The anterior and middle cerebral arterial flow was supplied through the communicating arteries. Congenital agenesis of the ICA was highly suspected, because the left carotid canal could not be discerned at all. The concurrence of agenesis of ICA with ipsilateral Homer syndrome is accounted for by simultaneous organogenesis of the carotid artery and cervical sympathetic nerve, both of which are derived from neural crest cells. Developmental anomalies of the cervical neural crest, though rare, should be included in the differential diagnosis of congenital Horner syndrome.View full abstractDownload PDF (1646K) -
[in Japanese], [in Japanese], [in Japanese], [in Japanese], [in Japane ...2007 Volume 39 Issue 1 Pages 66-67
Published: January 01, 2007
Released on J-STAGE: December 12, 2011
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[in Japanese], [in Japanese]2007 Volume 39 Issue 1 Pages 72-75
Published: January 01, 2007
Released on J-STAGE: December 15, 2011
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