Case 1: S. K. eight-year-old boy.
Treatment Manage and exercise forr straightening of the limbs.
Case 2: Y. M. new born female baby.
Died of pneumonia eighteen days after birth.
Case 3: S. Y. eighteen-year-old boy.
Treatment: Egger's operation of the knees and elongation of the achilles' tendons.
Case 4: N. A. three-year-old boy.
Died of shock three hours after surgery (Egger's operation of the left knee).
Case 5: N. F. twelve-year-old girl.
Treatment: Egger's operation of the knees and tripple arthrodesis of the Ankles.
Case 6: Y. K. thirteen-year-old boy.
Treatment: elongation of the achilles' tendons and Egger's operation of the knees.
Case 7: D. S. ten-year-old boy.
Treatment: tripple arthrodesis of the Ankles with elongation of the achilles' tendons.
Since 1958, seven cases of arthrogryposis multiplex congenita have been experienced. All of their mothers apparently had normal pregnancies, but three of the babies had difficulty in catching their first breath (syncope). All of them, however, showed some degree of “flexion contracture” of their limbs at birth. Four children showed symptoms of malnutrition when they were at the time of admission: six of them had unusually flaccid skin on their limbs; and all of them currently showed symptoms of “flexion contracture”. Two children showed a loss of mental ability (as expressed in I. Q. scores); two more had recurrent fits of epilepsia; and one had a synostosis of the cervical vertebrae.
The five survivors were given except the case 2 and 4.
The tests of electric reaction of degeneration showed negative results with respect to their degeneration, but there were several evidence of low excitability especially in the extensor muscles.
They were also given E. M. G. tests, four of them exhibited oscillograms characterized by low amplitude and irregularity, one patient exhibited extreme peak variations which seemed to show “synchronization voltage”.
Finally, braces were supplied to these patients who had been operated upon, in order to hold their limbs.
View full abstract