Histopathological study of the remnant of extrahepatic bile ducts in 50 cases of so-called uncorrectable biliary atresia, upon which we operated the last four years, has been performed. The histological findings of the remnant were classified into three types. Only two cases were found to have type Ia ducts in the porta hepatis area, from which we can expect better prognosis postoperatively. we also found that as the petients become older, the size of the duct in the remnant becomes smaller and the hepatic fibrosis becomes more remarkable. Therefore the operation should be performed in the infant with this lesion as young as possible. As for the evaluation of operative results of hepatic portoenterostomy for this lesion, a proper evaluation can be made only in these cases in which a microscopic examination of the remnant of extrahepatic bile duct at the porta hepatis area has been adequately performed.
Until now there have been only 8 cases reported of duplication of the rectum and/or anal canal including our case (1 5/12 girl). We discussed the embryological etiology and clinical features of this disease. This disease is a very rare malformation which is very interesting etiologically. When we notice the clinical features of constipation and gluteal tumor in children, we should bear in mind this disease.